Neurofibromatosis type 2: Hearing preservation and rehabilitation
نویسندگان
چکیده
منابع مشابه
[Possibility of hearing preservation treatment by patient suffered from neurofibromatosis type 2: case report].
The main tumor of cerebellopontine angle are vestibular schwannoma (80-90%). Most of them are unilateral lesion but 5% of them are bilateral pathological mass. There are genetic disease like neurofibromatosis type 1 and 2. According to National Institute of Heath Consensus Development Conference the best treatment method is microsurgery. The possibility of hearing preservation surgery give midd...
متن کاملCochlear implant in type 2 neurofibromatosis: an option for better hearing rehabilitation.
A neurofibromatose tipo 2 (NF2) é uma doença autossômica dominante com frequência de 0,5/100.0000 habitantes, manifestando-se principalmente por meio de schwannomas vestibulares bilaterais e perda auditiva profunda bilateral. Os implantes de tronco cerebral (ITC) têm sido o principal método de reabilitação auditiva nestes pacientes. Apesar de significar um enorme avanço no tratamento desses pac...
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INTRODUCTION Patients with neurofibromatosis type 2 (NF2) develop bilateral cochleovestibular schwannomas (CVSs) that cause binaural deafness in most individuals. Hearing loss occurs in an unpredictable manner and the underlying mechanisms are not known. To gain insight into the pathophysiologic basis for hearing loss in NF2, we performed a prospective cross-sectional study of untreated ears in...
متن کاملHearing improvement after bevacizumab in patients with neurofibromatosis type 2.
BACKGROUND Profound hearing loss is a serious complication of neurofibromatosis type 2, a genetic condition associated with bilateral vestibular schwannomas, benign tumors that arise from the eighth cranial nerve. There is no medical treatment for such tumors. METHODS We determined the expression pattern of vascular endothelial growth factor (VEGF) and three of its receptors, VEGFR-2, neuropi...
متن کاملHearing optimisation in neurofibromatosis type 2: A systematic review.
BACKGROUND It is common for patients with neurofibromatosis type 2 to develop bilateral profound hearing loss hearing loss, and this is one of the main determinants of quality of life in this patient group. OBJECTIVES The aim of this systematic review was to review the current literature regarding hearing outcomes of treatments for vestibular schwannomas in neurofibromatosis type 2 including ...
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ژورنال
عنوان ژورنال: Neurochirurgie
سال: 2018
ISSN: 0028-3770
DOI: 10.1016/j.neuchi.2018.09.003